Summary
Portal hypertension is a rare complication in hepatic amyloidosis. We experienced a case of a 40-year-old man with primary amyloidosis and advanced esophageal varices. Angiographic procedures clearly demonstrated portal hypertension secondary to intrahepatic arterio-portal shunting. Hepatic arterial embolization brought about a disappearance of the A-P shunt and portal hypertension, though rebleeding occured. To our knowledge, this is the first case report in which the pathogenesis of portal hypertension in hepatic amyloidosis was elucidated.
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Aramaki, T., Terada, H., Okumura, H. et al. Portal hypertension secondary to intrahepatic arterio-portal shunt in primary amyloidosis: A case report. Gastroenterol Jpn 24, 410–413 (1989). https://doi.org/10.1007/BF02774349
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DOI: https://doi.org/10.1007/BF02774349