The Indian Journal of Pediatrics

, Volume 60, Issue 4, pp 573–581 | Cite as

Clinico-hematological profile and natural history of childhood myelodysplastic syndromes

  • Gurjeevan Garewal
  • R. K. Marwaha
  • Ruma Ray
  • Neelam Marwaha
Original Articles

Abstract

The clinical and hematological characteristics of ten children with myelodysplastic syndromes diagnosed and followed up over a 3 year period are presented. All of them had anemia and a low platelet count whilst the white blood cell count was variable. Presentation with bilateral proptosis and acute febrile neutrophilic dermatosis (Sweet’s syndrome) were unique features observed in one case each. None of these cases could afford specific therapy and thus serve to illustrate the natural history of the disease in pediatric practice.

Key words

Myelodysplastic syndrome Sweet’s syndrome 

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Copyright information

© Dr. K C Chaudhuri Foundation 1993

Authors and Affiliations

  • Gurjeevan Garewal
    • 2
  • R. K. Marwaha
    • 1
  • Ruma Ray
    • 2
  • Neelam Marwaha
    • 2
  1. 1.Department of PediatricsPostgraduate Institute of Medical Education and ResearchChandigarh
  2. 2.Department of HematologyPostgraduate Institute of Medical Education and ResearchChandigarh

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