Conclusion
Angioedema associated with C1 INH deficiency requires diagnosis as soon as the first symptoms of the disease are manifest, and laboratory measurement of complement component levels at the least suspicion, in order to institute preventive and curative treatments. However, different clinical, laboratory, and genetic forms of this disease account for the diversity in the indications for treatment.
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Laurent, J., Guinnepain, MT. Angioedema associated with C1 inhibitor deficiency. Clinic Rev Allerg Immunol 17, 513–523 (1999). https://doi.org/10.1007/BF02737653
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DOI: https://doi.org/10.1007/BF02737653