Abstract
Stenotic lesion of the left coronary artery is an unnoticed but complicating feature of supravalvular aortic stenosis (SAS). We present successful repair of SAS with left coronary ostial stenosis. A 9-year-old girl was diagnosed as Williams syndrome associated with SAS. She had no symptoms of angina but cardiac catheterization revealed severe stenosis of the left coronary artery ostium. We adopted Brom’s three patch technique, which could enlarge the aortic root and ostial lesion of left coronary artery inclusively. This method is also ideal regarding restoration of the aortic root geometry.
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Iwase, J., Tajima, K., Io, A. et al. Successful repair of supravalvular aortic stenosis with ostial stenosis of the left coronary artery using Brom’s three patch technique. Jpn J Thorac Caridovasc Surg 51, 612–615 (2003). https://doi.org/10.1007/BF02736702
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DOI: https://doi.org/10.1007/BF02736702