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Hemophagocytic lymphohistiocytosis

Abstract

Hemophagocytic lymphohistiocytosis (HLH) is a rare condition in children associated with immunodeficiency, life threatening infections and malignancy. Infection associated hemophagocytosis responds well to appropriate antimicrobioal therapy and rarely to steroids when the infective agent is suspected to be of viral origin.

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Biswal, N., Shareef, S., Nalini, P. et al. Hemophagocytic lymphohistiocytosis. Indian J Pediatr 66, 632–635 (1999). https://doi.org/10.1007/BF02727184

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  • DOI: https://doi.org/10.1007/BF02727184

Key words

  • Hemophagocytosis
  • Infection associated hemophagocytosis (IAHS)
  • Familial erythrophagocitic lymphohistiocytosis (FEL)