Abstract
Mondini dysplasia with cerebrospinal fluid leak is a rare cause of recurrent pyogenic meningitis in children. We describe an eleven-year-old female child who presented with the fifth recurrent episode of pyogenic meningitis and unilateral sensorineural deafness. Mondini dysplasia of the inner ear with CSF-perilymph fistula was proven on an HRCT of the temporal bone and MRI. Successful operative intervention was undertaken to close the defect. Though rare, Mondini dysplasia should be considered as a cause of recurrent meningitis in children, especially if they have sensorineural deafness
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Tullu, M.S., Khanna, S.S., Kamat, J.R. et al. Mondini dysplasia and pyogenic meningitis. Indian J Pediatr 71, 655–657 (2004). https://doi.org/10.1007/BF02724130
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DOI: https://doi.org/10.1007/BF02724130