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OMENS-plus syndrome

The Indian Journal of Pediatrics volume 72, pages 707–708 (2005)Cite this article

Abstract

The OMENS syndrome involves craniofacial maldevelopment of theorbit, ear cranial nerve and soft tissue, while OMENS- plus syndrome also includes extracraniofacial anomalies. these may be skeletal, cardiovascular, gastrointestinal, pulmonary, renal and central nervous system malformations. A fourteen-year-old girl presented with hemifacial microsomia, digital abnormalities and pancreatitis. She was diagnosed as O1M2E0N2S1 - plus syndrome. Investigations revealed a type Ic choledochal cyst. the latter has not been reported as a gastrointestinal association earlier in literature to the best of the authors’ knowledge.

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Affiliations

  1. Senior Research Associate, Department of Pediatrics, Maulana Azad Medical College & Lok Nayak Hospital, 110002, New Delhi

    Seema Kapoor, S. B. Mukherjee, Ritu Paul & Bhavna Dhingra

Authors
  1. Seema Kapoor
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  2. S. B. Mukherjee
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  3. Ritu Paul
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  4. Bhavna Dhingra
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Correspondence to Seema Kapoor.

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Kapoor, S., Mukherjee, S.B., Paul, R. et al. OMENS-plus syndrome. Indian J Pediatr 72, 707–708 (2005). https://doi.org/10.1007/BF02724084

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  • DOI: https://doi.org/10.1007/BF02724084

Key words

  • OMENS plus syndrome
  • Choledochal cyst