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Subtotal colectomy and cecosigmoid anastomosis for colonie systemic sclerosis

Report of a case and review of the literature

  • Published:
Diseases of the Colon & Rectum

Purpose

We report a case of subtotal colonie involvement of systemic sclerosis, successfully managed by subtotal colectomy and cecosigmoid anastomosis, and review the literature on surgical management. METHODS: A patient had profound slow transit constipation and severe colonie involvement on nuclear transit study. Surgery was conservative, with preservation of distal sigmoid colon and the ileocecal valve. A literature search regarding management of colonie systemic sclerosis was conducted. RESULTS: The surgery was uncomplicated and near normal bowel function was restored. The literature indicates that colonie involvement is common in systemic sclerosis and that surgery is sometimes required for severe disease or the development of complications. CONCLUSIONS: If surgery is required for colonie involvement in systemic sclerosis, it should be directed at the segmental distribution of the disease, preserving the colon if possible and considering the possibility of concurrent small-bowel involvement. Nuclear colonie transit study is helpful in guiding the extent of surgery.

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Authors and Affiliations

  1. Colorectal Surgery Unit, Alfred Hospital, Melbourne, Australia

    Ian Lindsey R.A.C.S., Chip R. Farmer F.R.A.C.S. & Ian G. Cunningham F.R.A.C.S.

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  1. Ian Lindsey R.A.C.S.
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  2. Chip R. Farmer F.R.A.C.S.
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  3. Ian G. Cunningham F.R.A.C.S.
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Lindsey, I., Farmer, C.R. & Cunningham, I.G. Subtotal colectomy and cecosigmoid anastomosis for colonie systemic sclerosis. Dis Colon Rectum 46, 1706–1711 (2003). https://doi.org/10.1007/BF02660780

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