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Perianal alveolar rhabdomyosarcoma in a child

Report of a long-term survival case

  • Published:
Diseases of the Colon & Rectum

Abstract

The long-term survival of alveolar rhabdomyosarcoma of the perianal region in a 13-month-old infant is described. Local excision with chemotherapy consisting of vincristine, actinomycin D, and cyclophosphamide over a period of two years has resulted in eight years of tumor-free survival with normal growth and development. Our case and review of the literature suggest that local excision with chemotherapy may be an appropriate treatment for Group I perianal rhabdomyosarcoma in children.

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Mihara, S., Yano, H., Matsumoto, H. et al. Perianal alveolar rhabdomyosarcoma in a child. Dis Colon Rectum 26, 728–731 (1983). https://doi.org/10.1007/BF02554984

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  • DOI: https://doi.org/10.1007/BF02554984

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