Pediatric Cardiology

, Volume 17, Issue 1, pp 51–52 | Cite as

Sinus node dysfunction in tuberous sclerosis

  • C. G. Cowley
  • L. Y. Tani
  • V. E. Judd
  • R. E. Shaddy
Case Reports

Abstract

Tuberous sclerosis is an autosomal dominant disease with potential for involvement of the skin, brain, lungs, kidneys, and heart. A case of prolonged sinus node pause and episodes of unresponsiveness in a 21-week-old infant with tuberous sclerosis is described. The infant subsequently underwent placement of an epicardial pacemaker. This case illustrates the importance of electrocar-diographic studies in infants with tuberous sclerosis and seizure-like episodes.

Key words

Tuberous sclerosis Sinus node dysfunction 

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Copyright information

© Springer-Verlag New York Inc. 1996

Authors and Affiliations

  • C. G. Cowley
    • 1
    • 2
  • L. Y. Tani
    • 1
    • 2
  • V. E. Judd
    • 1
    • 2
  • R. E. Shaddy
    • 1
    • 2
  1. 1.Department of PediatricsPrimary Children’s Medical CenterSalt Lake CityUSA
  2. 2.University of Utah Medical CenterSalt Lake CityUSA

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