Pediatric Cardiology

, Volume 17, Issue 1, pp 35–39 | Cite as

Magnetic resonance imaging of absent pulmonary valve syndrome

  • H. Frank
  • U. Salzer
  • C. Popow
  • R. Stiglbauer
  • G. Wolleneck
  • H. Imhof
Case Reports

Abstract

A neonate with absent pulmonary valve syndrome was examined by means of echocardiography and magnetic resonance imaging (MRI). MRI provided an excellent evaluation of the intracrdial morphology, vessel anatomy, mediastinal structures, and shunt flow; and it was superior to echocardiography for detection of aortopulmonary collaterals and vessel abnormalities. This case report of an uncommon cardiac abnormality confirms that MRI is a useful complementary modality to echocardiography in neonates and is recommended for problems with central pulmonary vessels and their relation to tracheobronchial structures.

Key words

Absent pulmonary valve Echocardiography Magnetic resonance imaging Neonates 

Preview

Unable to display preview. Download preview PDF.

Unable to display preview. Download preview PDF.

References

  1. 1.
    Bove EL, Shaher RM, Alley R, McKneally M (1972) Tetralogy of Fallot with absent pulmonary valve and aneurysm of the pulmonary artery: report of two cases presenting as obstructive lung disease.J Pediatr 81:339–343PubMedCrossRefGoogle Scholar
  2. 2.
    Cheatham JP, Latson LA, Gutgesell HP (1982) Echocardiographic pulsed Doppler features of absent pulmonary valve syndrome in the neonate.Am J Cardiol 49:1773–1777PubMedCrossRefGoogle Scholar
  3. 3.
    Chevers N (1847) Recherches sur les maladies de l’artere pulmonaire,Arch Gen Med 15:488–508Google Scholar
  4. 4.
    Di Segni E, Einzig S, Bass JL, Edwards JE (1983) Congenital absence of pulmonary valve associated with tetralogy of Fallot: diagnosis by 2-dimensional echocardiography,Am J Cardiol 51:1798–1800PubMedCrossRefGoogle Scholar
  5. 5.
    Hamada R, Fukushima K, Oikawa T et al (1991) Absent pulmonary valve syndrome with tetralogy of Fallot: a rare radiographic presentation,Pediatr Cardiol 12:64–69PubMedCrossRefGoogle Scholar
  6. 6.
    Lakier JB, Stanger P, Heymann MA, Hoffmann JIE, Rudolph AM (1974) Tetralogy of Fallot with absent pulmonary valve: natural history and hemodynamic considerations.Circulation 50:167–175PubMedGoogle Scholar
  7. 7.
    Nagai Y, Komatsu Y, Nakamura K, Sato Y, Takao A (1979) Echocardiographic findings of congenital absence of the pulmonary valve with tetralogy of fallot.Chest 75:481–483PubMedGoogle Scholar
  8. 8.
    Pernot C, Hoeffel JC, Henry M, et al (1972) Radiological patterns of congenital absence of the pulmonary valve in infants.Radiology 102:619–622PubMedGoogle Scholar
  9. 9.
    Pinsky WW, Nihill MR, Mullins CE, Harrison G, McNamara DG (1978) The absent pulmonary valve syndrome.Circulation 57:159–162PubMedGoogle Scholar
  10. 10.
    Presbitero R, Pedretti E, Orzan F, et al (1984) Absent pulmonary valve syndrome with associated anomalies of the pulmonary blood supply.Int J Cardiol 6:587–596PubMedCrossRefGoogle Scholar
  11. 11.
    Rose J, Levin DC, Goldstein S, Laster W (1974) Congenital absence of the pulmonary valve associated with congenital aplasia of the thymus (DiGeorge’s syndrome).AJR Am J Roentgenol 122:97–102Google Scholar

Copyright information

© Springer-Verlag New York Inc. 1996

Authors and Affiliations

  • H. Frank
    • 1
  • U. Salzer
    • 2
  • C. Popow
    • 2
  • R. Stiglbauer
    • 3
  • G. Wolleneck
    • 4
  • H. Imhof
    • 3
  1. 1.Department of Internal Medicine II (Cardiology)University of ViennaViennaAustria
  2. 2.Department of PediatricsUniversity of ViennaViennaAustria
  3. 3.Magnetic Resonance InstituteUniversity of ViennaViennaAustria
  4. 4.Department of SurgeryUniversity of ViennaViennaAustria

Personalised recommendations