Brain Tumor Pathology

, Volume 16, Issue 2, pp 69–76 | Cite as

A case of endolymphatic sac tumor with long-term survival

  • Kenichiroh Asano
  • Tetsuji Sekiya
  • Toru Hatayama
  • Masahiko Tanaka
  • Atsuhito Takemura
  • Shigeharu Suzuki
  • Osami Kubo
  • Yoshihiro Ishihara
Case Report

Abstract

A 72-year-old man developed left facial palsy at age 14 and left-sided hearing loss at age 20. At the age of 59, he presented with gait disturbance, and a large left cerebellopontine angle tumor was detected, which had markedly destroyed the pyramidal bone. The tumor was subtotally resected, but he required two more operations at the ages of 64 and 69 because of tumor regrowth. At the present time, recurrent tumor has destroyed the occipital bone and is invading the scalp. However, eventhough he has several cranial nerve palsies and cerebellar ataxia, he remains in stable condition and demonstrates long-term survival. The patient's surgical specimens revealed a papillary adenoma, which was recently thought to be of endolymphatic sac origin, although the origin of this kind of tumor, whether arising from the middle ear or from the endolymphatic sac, has not been established with certainty so far. In this paper, we provide further evidence that this tumor originates from the endolymphatic sac, based on anatomical, histopathological, and embryological evidence.

Key words

Endolymphatic sac tumor Adenoma Papillary structure Immunohistochemistry Long-term survival 

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Copyright information

© The Japan Society of Brain Tumor Pathology 1999

Authors and Affiliations

  • Kenichiroh Asano
    • 1
  • Tetsuji Sekiya
    • 1
  • Toru Hatayama
    • 1
  • Masahiko Tanaka
    • 1
  • Atsuhito Takemura
    • 1
  • Shigeharu Suzuki
    • 1
  • Osami Kubo
    • 2
  • Yoshihiro Ishihara
    • 3
  1. 1.Department of NeurosurgeryHirosaki University, School of MedicineHirosaki, Aomori PrefectureJapan
  2. 2.Department of Neurosurgery, Neurological InstituteTokyo Women's Medical CollegeTokyoJapan
  3. 3.Gerlatric Health Faculties Machida-SakuranboTokyoJapan

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