Abstract
A rare case of the segmental type of primary sclerosing cholangitis (PSC) is reported herein. A 27 year old Japanese man with obstructive jaundice was referred to our hospital with a provisional diagnosis of bile duct cancer at the hepatic hilum. A PTCD tube had been inserted from the right anterior segmental duct and direct cholangiograms showed complete obstruction of the bile duct at the confluence of the right and left hepatic ducts. Resection of the extrahepatic bile duct and partial hepatectomy were thus performed, however, the postoperative histological examination revealed no malignant features. Instead, the lesion was shown to be compatible with PSC microscopically. A diagnosis of PSC was finally established on the basis of clinical features, cholangiographic appearance and the pathological report.
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Helzberg JH, Petersen JM, Boyer JL. Improved survival with primary sclerosing cholangitis. Gastroenterology 1987; 92: 1869–1875.
Schrumpf E, Fausa O, Kolmannskog F, Elgjo K, Ritland S, Gjone E. Sclerosing cholangitis in ulcerative colitis: a follow-up study. Scand J Gastroenterol 1982; 17: 33–39.
Furukawa H, Kikuchi T, Taniguchi T, Hara S, Ryu M. A case report of primary sclerosing cholangitis—A review of Japanese literature. Nippon Shokaki Geka Gakkai Zasshi (Jpn J Gastroenterol Surg) 1984; 17: 1883–1886. (in Japanese)
Caroli J, Rosner D. Chronic sclerosing cholangitis. In: Bockus HK. ed. Gastroenterology, Vol. 3. Philadelphia: WB Saunders 1976; 868–873.
Sugita T, Hatano H, Hanaoka M, Tominaga S, Sakaguchi S, Kitami Y, Ishida T. Two cases of primary sclerosing cholangitis. Geka Shinryo (Geka Shinryo) 1973; 15: 737–742. (in Japanese)
Beppu M, Horikawa S, Hikita K, Kurita K, Hirai T, Murai N, Taniguchi S, Yoshimoto S, Doi Y, Uehara N, Ohta T. Primary sclerosing cholangitis—A case report. Nippon Shokakibyo Gakkai Zasshi (Jpn J Gastroent) 1976; 73: 1590–1598. (in Japanese)
Kawamura S, Nagadomi Y, Harada T, Fuji T, Shimizu M, Kodama T, Okamoto Y, Noda K, Mizuta M, Takemoto T. The interesting retrograde cholangiographic appearance of primary sclerosing cholangitis and other similar diseases. Nippon Shokaki Naishikyo Gakkai Zasshi (Gastroenterol Endoscopy) 1977; 19: 140–148. (in Japanese)
Yoshikawa S, Nakaba H, Sasako Y, Nishigaki K, Maeda G, Saya M. A case of primary sclerosing cholangitis treated by left hepatic lobectomy and right intrahepaticojejunostomy. Geka Shinryo (Geka Shinryo) 1982; 24: 223–227. (in Japanese)
Narai S, Otsuka T, Sato T, Imaizumi S, Kuribayashi K, Sato Y, Yoshida K, Yamagiwa I. A case of segmental sclerosing cholangitis. Nippon Rinsho Geka Igakkai Zasshi (Journal of Japanese Society for Clinical Surgery) 1982; 12: 1356–1361. (in Japanese)
Ito N, Oishi A, Tameda Y, Kosaka Y, Takezawa H, Yatani R, Miyake T, Hamaguchi K. Primary sclerosing cholangitis: Reports of two autopsied cases and review of fifty-one cases reported in Japan. Kanzo (Acta Hepatologica Japonica) 1982; 23: 1184–1192. (in Japanese)
Nara N, Bizen R, Uemura S, Sousetsu T, Kudoh T. A case of primary sclerosing cholangitis mimicking bile duct cancer. Naika (Internal Medicine) 1982; 49: 179–182. (in Japanese)
Suzuki N, Machi Y, Hirohashi K, Kinoshita H, Sakai K, Kobayashi Y. A case report of primary sclerosing cholangitis. Shokaki Geka (Gastroenterological Surgery) 1984; 7: 621–624. (in Japanese)
Hirata S, Sasaki N, Inoue K, Kawaguchi M, Mutou H, Orihashi K, Gomyo Y, Ohe K. A case report of localized primary slcerosing cholangitis mimicking choledochal cancer. Nippon Rinsho Geka Igakkai Zasshi (Journal of Japanese Society for Clinical Surgery) 1986; 47: 1334–1340. (in Japanese)
Nakagawa H, Nakagou R, Ohyama M, Yoshida E, Kobayashi T, Kurokawa T, Manabe T, Kobayashi S. A case of localized, primary sclerosing cholangitis difficult to differentiate from cholangiocarcinoma. Nippon Rinsho Geka Igakkai Zasshi (Journal of Japanese Society for Clinical Surgery) 1988; 49: 892–898. (in Japanese)
Thompson HH, Pitt HA, Tompkins RK, Longmire WP Jr. Primary sclerosing cholangitis—A heterogeneous disease. Ann Surg 1982; 196: 127–136.
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Tsunoda, T., Eto, T., Yamada, M. et al. Segmental primary sclerosing cholangitis mimicking bile duct cancer—Report of a case and review of the Japanese literature. The Japanese Journal of Surgery 21, 329–334 (1991). https://doi.org/10.1007/BF02470955
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DOI: https://doi.org/10.1007/BF02470955