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Gastrectomy in siblings with christmas disease (Hemophilia B)

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Abstract

Gastrointestinal hemorrhage is regarded as one of the commonest clinical manifestations of classic hemophilia and Christmas disease. Although major surgery is usually avoided in such cases, recently we had 2 cases of Christmas disease in siblings who had undergone a successful gast-rectomy and concomitant administration of a concentrated preparation of factor IX. In addition, findings in 7 other Japanese patients with hemophilia who underwent gastrectomy are discussed.

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Mizumoto, R., Kawarada, Y. & Ogura, Y. Gastrectomy in siblings with christmas disease (Hemophilia B). The Japanese Journal of Surgery 10, 328–337 (1980). https://doi.org/10.1007/BF02468796

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