Pediatric Cardiology

, Volume 5, Issue 3, pp 191–195 | Cite as

Retroesophageal right aortic arch

  • Adam Schneeweiss
  • Leonard Blieden
  • Abraham Shem-Tov
  • Victor Deutsch
  • Henry N. Neufeld
Original Article


Right aortic arch with left descending aorta and a retroesophageal aortic segment is an uncommon congenital vascular malformation which may cause symptoms of compression from a vascular “ring.” The presence of this malformation may be suspected by the findings on barium swallow and the diagnosis confirmed by angiocardiography. Surgical intervention may be necessary in patients who have severe symptoms.

Key words

Right retroesophageal aortic arch Tetralogy of Fallot Aberrant left subclavian artery Mirror-image pattern Vascular ring 


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  1. 1.
    Blieden LC, Schneeweiss A, Deutsch V, Neufeld HN (1978) Right aortic arch with left descending aorta (circumflex aorta): roentgenographic diagnosis.Pediatr Radiol 6:208–210PubMedCrossRefGoogle Scholar
  2. 2.
    Dominguez R, Sang Oh K, Dorst JP, Young LW (1978) Left aortic arch with right descending aorta.Am J Roentgenol 130:917–920Google Scholar
  3. 3.
    Edwards JE (1948) Retro-oesophageal segment of the left aortic arch, right ligamentum arteriosum and right descending aorta, causing congenital vascular ring about the trachea and oesophagus.Proc Mayo Clin 23:108–119Google Scholar
  4. 4.
    Edwards JE (1948) Anomalies of the derivations of the aortic arch system.Med Clin North Am 32:925–949Google Scholar
  5. 5.
    Felson B, Palagew MJ (1963) The two types of right aortic arch.Radiology 81:745–759PubMedGoogle Scholar
  6. 6.
    Hastreiter AR, d'Cruz JA, Canter T (1966) Right-sided aorta.Br Heart J 28:722–739PubMedGoogle Scholar
  7. 7.
    Heim de Balsac R (1960) Left aortic arch (posterior or circumflex type) with right descending aorta.Am J Cardiol 5:546–550CrossRefGoogle Scholar
  8. 8.
    Heinrich WD, Perer Tamago R (1956) Left aortic arch and right descending aorta: case report.Am J Roentgenol 76:762–769Google Scholar
  9. 9.
    Knight L, Edwards JE (1974) Right aortic arch: types and associated cardiac anomalies.Circulation 50:1047–1051PubMedGoogle Scholar
  10. 10.
    Murthy K, Mattioli L, Diehl AM, Holder TM (1970) Vascular ring due to left aortic arch, right descending aorta and right patent ductus arteriosus.J Pediatr Surg 5:550–554PubMedCrossRefGoogle Scholar
  11. 11.
    Park SC, Siewers RD, Lenox WNH, Zuberbuhler JR (1976) Left aortic arch with right descending aorta and right ligamentum arteriosum.J Thorac Cardiovasc Surg 71:779–784PubMedGoogle Scholar
  12. 12.
    Pattinson JN, Emanuel RW (1957) The aorta and pulmonary arteries in Fallots tetralogy.Br Heart J 19:201–205PubMedGoogle Scholar
  13. 13.
    Paul RN (1948) A new anomaly of the aorta: left aortic arch with right descending aorta.J Pediatr 32:19–39CrossRefGoogle Scholar
  14. 14.
    Schlamowitz ST, Di Giorgi S, Gensini GG (1962) Left aortic arch and right descending aorta.Am J Cardiol 10:132–137PubMedCrossRefGoogle Scholar
  15. 15.
    Shuford WH, Sybers RG (1974)The aortic arch and its malformations, 1st edn. Charles C Thomas, Springfield ILGoogle Scholar
  16. 16.
    Sterz H (1961) Dysphagia durch eine seltere Anomalie der Aorta Thoracalis: Arcus Aortae Sinister Circumflex and Dextroposition der Aorta Descendens.Wien Z Inn Med 42:420–429PubMedGoogle Scholar
  17. 17.
    Stewart JR, Kincaid OW, Edwards JE (1967)An atlas of vascular rings and related malformations of the aortic arch system. Charles C Thomas, Springfield, IL, pp 3–9Google Scholar
  18. 18.
    Young SS, Maraanhao V, Goldberg H (1965) Left aortic arch and right descending aorta.Lancet 85:133–135Google Scholar

Copyright information

© Springer-Verlag 1984

Authors and Affiliations

  • Adam Schneeweiss
    • 1
  • Leonard Blieden
    • 2
  • Abraham Shem-Tov
    • 1
  • Victor Deutsch
    • 1
  • Henry N. Neufeld
    • 1
  1. 1.Heart InstituteChaim Sheba Medical CenterTel Hashomer
  2. 2.Bellinson HospitalMassada Center for Heart DiseasePetach TikvaIsrael

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