Summary
A review of 18 cases with discrete suboartic stenosis (DSS) revealed that involvement of the aortic valve cusps in the basic process was present in 16. In these 16 cases, extensions of fibroelastic tissue from the site of the DSS toward the base or superior to the base of one or more cusps were seen. In seven of the involved cases, deformity of a cusp was associated with these extensions. Valvular aortic insufficiency in cases with DSS might be caused by extensions of the fibroelastic tissue to the aortic cusps.
References
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This study was supported by research grant 5 RO1 HL05694 from the National Heart, Lung, and Blood Institute, National Institutes of Health, Bethesda, Maryland, and by the Dwan Family Fund.
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Feigl, A., Feigl, D., Lucas, R.V. et al. Involvement of the aortic valve cusps in discrete subaortic stenosis. Pediatr Cardiol 5, 185–189 (1984). https://doi.org/10.1007/BF02427043
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DOI: https://doi.org/10.1007/BF02427043