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Interruption of the aortic arch with aorticopulmonary septal defect

An anatomic review

  • Anatomic Review
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Summary

Interruption of the aortic arch may occur with aorticopulmonary septal defect (APSD) as part of a developmental complex. The anatomic details of 46 cases of interruption of the aortic arch with APSD revealed the following characteristics: (1) type A interruption of the aortic arch occurred nearly six times more commonly than type B interruption; (2) the APSD was variable in size and position, conforming to the types previously described; (3) the ventricular septum was usually intact, but a ventricular septal defect was present in six cases and occurred more frequently with type B interruption of the aortic arch; (4) subaortic stenosis was not present in any of the 16 cases in which adequate details were available to make a judgment.

The association of APSD with interruption of the aortic arch in infancy is not uncommon. Evaluation of infants with APSD should thus include evaluation of the aortic arch. The occurrence of interruption of the aortic arch with an intact ventricular septum is distinctly unusual. In such cases an APSD should be suspected and sought.

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Authors and Affiliations

  1. Departments of Pathology, United Hospitals, St. Paul, Minnesota

    Elizabeth Braunlin, William M. Peoples, Robert M. Freedom, Donald C. Fyler, Allan Goldblatt & Jesse E. Edwards

  2. University of Minnesota, Minneapolis, Minnesota

    Elizabeth Braunlin, William M. Peoples, Robert M. Freedom, Donald C. Fyler, Allan Goldblatt & Jesse E. Edwards

  3. Departments of Pediatric Cardiology, University of Minnesota, Minneapolis

    Elizabeth Braunlin, William M. Peoples, Robert M. Freedom, Donald C. Fyler, Allan Goldblatt & Jesse E. Edwards

  4. St. Joseph's Hospital, Phoenix, Arizona

    Elizabeth Braunlin, William M. Peoples, Robert M. Freedom, Donald C. Fyler, Allan Goldblatt & Jesse E. Edwards

  5. The Hospital for Sick Children, Toronto, Ontario

    Elizabeth Braunlin, William M. Peoples, Robert M. Freedom, Donald C. Fyler, Allan Goldblatt & Jesse E. Edwards

  6. The Children's Hospital Medical Center, Boston, Massachusetts

    Elizabeth Braunlin, William M. Peoples, Robert M. Freedom, Donald C. Fyler, Allan Goldblatt & Jesse E. Edwards

  7. Massachusetts General Hospital, Boston

    Elizabeth Braunlin, William M. Peoples, Robert M. Freedom, Donald C. Fyler, Allan Goldblatt & Jesse E. Edwards

Authors
  1. Elizabeth Braunlin
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  2. William M. Peoples
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  3. Robert M. Freedom
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  4. Donald C. Fyler
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  5. Allan Goldblatt
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  6. Jesse E. Edwards
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Additional information

Supported by Public Health Service research grants 5 RO1 HL 05694 and 5 T32 HL07359 from the National Heart, Lung, and Blood Institute

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Braunlin, E., Peoples, W.M., Freedom, R.M. et al. Interruption of the aortic arch with aorticopulmonary septal defect. Pediatr Cardiol 3, 329–335 (1982). https://doi.org/10.1007/BF02427036

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