Pediatric Cardiology

, Volume 3, Issue 4, pp 315–318 | Cite as

Criss-cross heart with discordant atrioventricular connections

  • Bruno Marino
  • Luigi Chiariello
  • Cesare Bosman
  • Federico Marsico
  • Raffaele Calabro
  • Attilio Reale
  • Benedetto Marion


A case of criss-cross heart is presented in which there was situs solitus with atrioventricular (AV) discordance and single outlet, the aorta arising from the right ventricle. Associated lesions were pulmonary atresia and ventricular septal defect.

The apparently normal AV relation in the presence of a discordant AV connection can be explained by the hypothesis that an embryonic 1-bulboventricular loop developed and was followed by marked counter-clockwise rotation of the ventricles.

Key words

Embryology Pulmonary atresia Atrioventricular (AV) connections Congenital heart disease 


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Copyright information

© Springer-Verlag New York Inc 1982

Authors and Affiliations

  • Bruno Marino
    • 1
  • Luigi Chiariello
    • 2
  • Cesare Bosman
    • 3
  • Federico Marsico
    • 4
  • Raffaele Calabro
    • 4
  • Attilio Reale
    • 1
  • Benedetto Marion
    • 5
  1. 1.Department of CardiologyUniversity of RomeItaly
  2. 2.Department of Cardiac SurgeryUniversity of PisaItaly
  3. 3.Department of PathologyUniversity of RomeItaly
  4. 4.Department of CardiologyPausilipon HospitalNaplesItaly
  5. 5.Department of Cardiac SurgeryUniversity of RomeItaly

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