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Pediatric Cardiology

, Volume 2, Issue 4, pp 323–328 | Cite as

Successful excision of an atrial fibroma in a four-month-old male infant

  • Monica Rutkowski
  • Eugenie F. Doyle
  • Delores Danilowicz
  • M. Alba Greco
  • O. Wayne Isom
Article

Summary

This report presents an infant who was initially admitted with a pericardial effusion. Subsequent evaluation led to the diagnosis of a primary cardiac tumor. Excision of the tumor which arose from the atrial septum was possible only by removing most of the free right atrial wall and a portion of the septal leaflet of the tricuspid valve. Reconstruction of the tricuspid valve leaflet by reattachment of chordae and a partial annuloplasty was done with the right atrial wall being replaced using pericardial tissue. The histology of the tumor was compatible with a fibroma, a type not previously reported in this location in the pediatric age group. Twenty-one months following operation, the child was restudied and the catheterization revealed mild to moderate tricuspid regurgitation and no recurrence of the tumor. The child is now 4 years of age and remains asymptomatic with normal growth and development and no evidence of fibromatosis.

Key words

Atrial tumor Cardiac tumors Fibroma Pericardial effusion 

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Copyright information

© Springer-Verlag New York Inc 1982

Authors and Affiliations

  • Monica Rutkowski
    • 1
  • Eugenie F. Doyle
    • 1
  • Delores Danilowicz
    • 1
  • M. Alba Greco
    • 1
  • O. Wayne Isom
    • 1
  1. 1.Departments of Pediatrics, Pathology and SurgeryNew York University Medical CenterNew York

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