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Direct entry of the right superior vena cava into the left atrium with aneurysmal dilatation and stenosis at its entry into the right atrium with stenosis of the pulmonary veins: A rare case

Pediatric Cardiology volume 5, pages 123–126 (1984)Cite this article

Summary

This is the first autopsied case reported in the English language literature wherein the right superior vena cava entered both atria with obstruction of the entry into the right atrium, aneurysmal dilatation of the proximal part of the superior vena cava, and entry of the stenosed right upper pulmonary vein into the aneurysmal sac. The aneurysmally dilated right superior vena cava communicated directly with the left atrium. In addition, the remainder of the pulmonary veins, all of which were markedly stenosed, entered the left atrium. The embryogenesis of this unique malformation is briefly discussed.

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Affiliations

  1. Congenital Heart and Conduction System Laboratory, Department of Pathology, Deborah Heart and Lung Center, Browns Mills, New Jersey

    Saroja Bharati & Maurice Lev

  2. Department of Pathology, Temple University, Philadelphia

    Saroja Bharati & Maurice Lev

  3. Department of Pathology, Pennsylvania State University, Milton S. Hershey Medical Center, Hershey, Pennsylvania, USA

    Saroja Bharati & Maurice Lev

Authors
  1. Saroja Bharati
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  2. Maurice Lev
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Aided by grant HL 30558-01 from the National Heart, Lung and Blood Institute of the National Institutes of Health, Bethesda, Maryland.

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Bharati, S., Lev, M. Direct entry of the right superior vena cava into the left atrium with aneurysmal dilatation and stenosis at its entry into the right atrium with stenosis of the pulmonary veins: A rare case. Pediatr Cardiol 5, 123–126 (1984). https://doi.org/10.1007/BF02424964

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  • DOI: https://doi.org/10.1007/BF02424964

Key words

  • Entry of right superior vena cava into both atria
  • Pulmonary vein stenosis
  • Anomalous pulmonary venous drainage (partial)
  • Anomalous systemic venous drainage