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Pediatric Radiology

, Volume 15, Issue 4, pp 225–228 | Cite as

Narrow trachea in mucopolysaccharidoses

  • M. E. Peters
  • S. Arya
  • L. O. Langer
  • E. F. Gilbert
  • R. Carlson
  • W. Adkins
Originals

Abstract

Nine of 56 patients with mucopolysaccharidoses (MPS) showed small tracheal diameters on their frontal chest radiographs. Autopsy of an MPS I-H (Hurler disease) patient demonstrated that the small calibre was secondary to deposition of glycosaminoglycan (mucopolysaccharide). Autopsies of two patients with other storage diseases, one with geleophysic dysplasia and one with mucolipidosis II, also exhibited compromise of their airways because of storage material accumulation.

Keywords

Public Health Chest Radiograph Glycosaminoglycan Storage Disease Storage Material 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© Springer-Verlag 1985

Authors and Affiliations

  • M. E. Peters
    • 2
  • S. Arya
    • 2
  • L. O. Langer
    • 2
  • E. F. Gilbert
    • 2
  • R. Carlson
    • 2
  • W. Adkins
    • 1
  1. 1.Central Wisconsin Center for the Developmentally DisabledMadisonUSA
  2. 2.Dr. Mary Ellen Peters Department of RadiologyUniversity of Wisconsin Clinical Science CenterMadisonUSA

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