Abstract
We report the waking and sleeping polygraphic and evoked potential data recorded during the follow-up of a child with chronic progressive epilepsia partialis continua of childhood (Bancaud's type II). The findings that emerged from these investigations coupled with the clinical pattern enabled us to delineate the course of this rare condition and provided clues for a tentative interpretation of the pathogenesis of the repetitive myoclonic jerks typical of epilepsia partialis continua, on which there is as yet no consensus. In our case involvement of cortico-subcortical systems seems probable.
Sommario
Gli AA. riportano i dati neurofisiologici ottenuti con registrazioni poligrafiche in veglia, polisonnografie e potenziali evocati, durante il follow-up di un bambino affetto da epilessia parziale continua cronica e progressiva dell'infanzia (forma II di Bancaud). I particolari reperti emersi da queste indagini associati al quadro clinico, oltre che delineare l'andamento di questa rara forma morbosa, offrono lo spunto per tentare di interpretare la patogenesi delle mioclonie ripetitive tipiche della E. parziale continua, per la quale non sussiste un accordo in letteratura. Nel nostro caso sembra ipotizzabile un coinvolgimento di sistemi cortico-sottocorticali.
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Perniola, T., Sforza, E., Rodriguez, M. et al. Neurophysiological follow-up in a case of chronic progressive epilepsia partialis continua of childhood. Ital J Neuro Sci 10, 369–376 (1989). https://doi.org/10.1007/BF02333785
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DOI: https://doi.org/10.1007/BF02333785