Abstract
A man who had had an episode of localized encephalitis, diagnosed as viral cerebellitis in childhood came to observation at the age of 23 for attacks of segmental myoclonus of the cervical axial musculature. BAEP changes at brainstem level in this case point to involvement of the Guillain-Mollaret triangle in the pathogenesis of this syndrome.
Sommario
Un paziente, colpito in età infantile da un episodio di encefalite localizzata diagnosticata come cerebellite virale, giunse alla nostra osservazione all'età di 23 a. per degli accessi di mioclonie segmentali a carico della muscolatura assiale cervicale. Le alterazioni dei BAEPs a livello del tronco cerebrale, registrate in tal caso, ci fanno propendere per un coinvolgimento del triangolo di Guillain-Mollaret nella patogenesi di tale sindrome.
Similar content being viewed by others
References
Avanzini G., Beluffi M., Caracent T., Leone B.:Mioclonie ritmiche scheletriche in corso di neurinoma dell'acustico. Rivista di Neurobiologia XVI 4:644–656, 1968.
Fahn S., Marsden D.C., Van Woert M.:Definition and classification of myoclonus pp. 1–5 in Advances in Neurology. Myoclonus vol. 43 Ed. Fahn, Marsden, Van Woert. New York Raven Press 1986.
Garcin R., Lapresle J., Fardean M.:Myoconies squelettiques rythmées sans nystagmus du voile. Rev Neurol 109:105–14, 1963.
Hallet M.:The pathophysiology of myoclonus. Trend Neurosc 10:69–73, 1987.
Halliday A.M.:The electrophysiological study of myoclonus in man. Brain 90:241–284, 1967.
Jacobs L., Newman P.R., Bozian D.:Disoppearing palatal myoclonus. Neurology 31:748–51, 1981.
Lapresle J.:Palatal myoclonus, pp. 265–73 in: Advances in Neurology. Myoclonus, vol. 43, Ed. Fahn, Marsden, Van Woert. New York, Raven Press 1986.
Marsden C.D., Hallett M., Fahn S.:The nosology and pathophysiology of myoclonus, pp 196–248 in: Butterworths International Medical Review. Movement Disorders vol. 2, 1982.
Shibasaki H., Kuroiwa Y.:Electroencephalographic correlates of myoclonus. Electroenceph clin Neurophysiol 39: 455–463, 1975.
Sperling R.M., Hermann C.:Syndrome of palatal myoclonus and progressive ataxia: two cases with magnetic resonance imaging. Neurology 35:1212–1214, 1985.
Author information
Authors and Affiliations
Rights and permissions
About this article
Cite this article
Costa, B., Tacconi, P., Pinna, L. et al. Segmental myoclonus in a young man who had had localized encephalitis in childhood. Ital J Neuro Sci 10, 357–359 (1989). https://doi.org/10.1007/BF02333783
Issue Date:
DOI: https://doi.org/10.1007/BF02333783