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Pediatric Cardiology

, Volume 3, Issue 2, pp 153–159 | Cite as

Restrictive cardiomyopathy with pseudotumor formation of the left ventricle

  • Richard A. Schieber
  • Paul R. Lurie
  • Harry B. Neustein
Case Reports

Summary

A 4-year-old girl had the insidious onset of congestive heart failure without apparent cause. Evaluation by echocardiography, thallous chloride Tl 201 scintigraphy, and angiography suggested the presence of either a neoplasm or restrictive cardiomyopathy with a localized mass effect on the left ventricle. Pathological specimens obtained by transvascular endomyocardial biopsy and at surgery defined the pathology to be restrictive cardiomyopathy. Analysis of myocardium by electron microscopy demonstrated a previously undescribed abnormality of the contractile elements involving the myofilaments and Z bands, with generalized secondary glycogen deposition.

Key words

Restrictive cardiomyopathy Cardiac tumor Endomyocardial biopsy 

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Copyright information

© Springer-Verlag New York Inc 1982

Authors and Affiliations

  • Richard A. Schieber
    • 1
    • 2
  • Paul R. Lurie
    • 1
    • 2
  • Harry B. Neustein
    • 1
    • 2
  1. 1.Division of Cardiology and Department of PathologyChildrens Hospital of Los AngelesLos Angeles
  2. 2.Departments of Pediatrics and PathologyUniversity of Southern California School of MedicineLos Angeles

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