Neuroradiology

, Volume 38, Supplement 1, pp S196–S199 | Cite as

MRI in an unusual case of congenital spinal mesenchymal proliferation

  • P. Tortori-Donati
  • M. P. Fondelli
  • A. Rossi
  • L. Andreussi
  • M. Brisigotti
  • M. L. Garrè
Paediatric Neuroradiology

Abstract

We report a child aged 2 years. presenting with delayed motor development. A thoracolumbar subcutaneous mass was noticed in the first months of life. MRI showed a low conus medullaris, confirmed the presence of the mass and detected a second solid lesion in the intradural space. Surgery confirmed that the two lesions were distinct, as on MRI. The histopathological features were in common with fibrous hamartoma of infancy, giant cell angioblastoma and the “diffuse type” of infantile fibromatosis. The presence of a low conus medullaris associated with a congenital clinical presentation suggested a disontogenetic aetiology.

Key words

Angioblastoma Fibromatosis Hamartoma Magnetic resonance imaging Spinal tumours Children 

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Copyright information

© Springer-Verlag 1996

Authors and Affiliations

  • P. Tortori-Donati
    • 1
  • M. P. Fondelli
    • 1
  • A. Rossi
    • 1
  • L. Andreussi
    • 2
  • M. Brisigotti
    • 3
  • M. L. Garrè
    • 4
  1. 1.Department of NeuroradiologyChildren's Hospital “G. Gaslini”GenoaItaly
  2. 2.Department of NeurosurgeryChildren's Hospital “G. Gaslini”GenoaItaly
  3. 3.Department of PathologyGeneral Hospital of BresciaItaly
  4. 4.Department of OncologyChildren's Hospital “G. Gaslini”GenoaItaly

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