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Neuroradiology

, Volume 38, Supplement 1, pp S165–S168 | Cite as

Desmoplastic supratentorial neuroepithelial tumours of childhood: Imaging in 5 patients

  • F. Rypens
  • M. J. Esteban
  • J. Baraton
  • F. Brunelle
  • A. Lellouch-Tubiana
  • C. Bastien-Fagnou
  • D. Renier
Paediatric Neuroradiology

Abstract

Desmoplastic neuroepithelial tumours are rare supratentorial neoplasms of infancy with a favourable prognosis. We characterised their imaging findings by reviewing the clinical and radiological reports of five affected children. The tumours were massive, predominantly cystic and with preferential frontal and parietal lobe involvement. The cystic component was in the white matter, with no communication with the ventricle. The solid part was superficially, abutting a meningeal surface, and showed intense contrast enhancement. A heterogeneous predominantly solid mass was observed in one patient. Thinning and deformation of the skull adjacent to the tumour was shown in four cases. Peritumoral oedema was absent or moderate. No calcification or haemorrhage were present. Angiography showed a tumour blush from the internal or external carotid arteries in one case each. Follow-up (3 months-9 years, mean 4.5 years) showed no recurrence.

Key words

Neuroepithelial tumor of childhood, supratentorial Desmoplastic astrocytoma Desmoplastic ganglioglioma Magnetic resonance imaging Computed tomography 

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Copyright information

© Springer-Verlag 1996

Authors and Affiliations

  • F. Rypens
    • 1
  • M. J. Esteban
    • 1
  • J. Baraton
    • 1
  • F. Brunelle
    • 1
  • A. Lellouch-Tubiana
    • 2
  • C. Bastien-Fagnou
    • 3
  • D. Renier
    • 4
  1. 1.Department of RadiologyHôpital des Enfants MaladesParis Cedex 15France
  2. 2.Department of PathologyHôpital des Enfants MaladesParis Cedex 15France
  3. 3.Department of RadiologyHôpital TrousseauParisFrance
  4. 4.Department of NeurosurgeryHôpital des Enfants MaladesParis Cedex 15France

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