Summary
The association between cutaneous vasculitis and lymphoproliferative disease has been increasingly recognized. We report a female patient who presented with cutaneous vasculitis which was due to a small cell pleomorphic T-cell lymphoma. In spite of aggressive therapy, she died two years after onset of disease. The clinical picture of vasculitis associated with lympho-proliferative disease is addressed with particular emphasis on symptoms and signs suggesting malignancy rather than vasculitis appearing in concert with well-defined connective tissue disorders.
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Gran, J.T., Sund, S. & Langholm, R. Small cell pleomorphic T-cell lymphoma presenting with cutaneous vasculitis. Clin Rheumatol 13, 628–630 (1994). https://doi.org/10.1007/BF02243007
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DOI: https://doi.org/10.1007/BF02243007