Omphalocele associated with coronary sinus atrial septal defect: Report of two cases

Summary

Two children with omphalocele were found to have coronary sinus atrial septal defect as part of their congenital heart disease complex. This unusual atrial communication may elude preoperative detection unless specifically sought. Its occurrence in conjunction with omphalocele may represent more than a chance association.

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References

  1. 1.

    Aitken J (1963) Exomphalos, analysis of a 10-year series of 32 cases.Arch Dis Child 38:126–129

    Google Scholar 

  2. 2.

    Bunger PC, Neufeld DA, Moore JC et al. (1981) Persistent left superior vena cava and associated structural and functional considerations.Angiology 32:601–608

    Google Scholar 

  3. 3.

    Duhamel B (1963) Embryology of exomphalos and allied malformations.Arch Dis Child 38:142–147

    Google Scholar 

  4. 4.

    Greenwood RD, Rosenthal A, Nadas AS (1974) Cardiovascular malformations associated with omphalocele.J Pediatr 85:818–821

    Google Scholar 

  5. 5.

    Jones PG (1963) Exomphalos (syn. omphalocele), a review of 45 cases.Arch Dis Child 38:180–187

    Google Scholar 

  6. 6.

    Mantini E, Rondin CM, Lillihei CW, et al. (1966) Congenital circulation anomalies involving the coronary sinus.Circ 33:317–327

    Google Scholar 

  7. 7.

    Quaegebeur J, Kirklin JW, Pacifico AD, et al. (1979) Surgical experience with unroofed coronary sinus.Ann Thorac Surg 27:418–425

    Google Scholar 

  8. 8.

    Raghib G, Ruttenberg HD, Anderson RC, et al. (1965) Termination of left superior vena cava in left atrium, atrial septal defect, and absence of coronary sinus.Circ, 31:906–918

    Google Scholar 

  9. 9.

    Sand ME, McGrath LB, Pacifico AD, et al. (1986) Repair of left superior vena cava entering the left atrium.Ann Thorac Surg 42:560–564

    Google Scholar 

  10. 10.

    Smith WR, Leix F (1966) Omphalocele.Am J Surg 111:450–456

    Google Scholar 

  11. 11.

    Winter FS (1954) Persistent left superior vena cava: Survey of the world literature and report of thirty additional cases.Angiology 5:90–132

    Google Scholar 

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Correspondence to Dr. Carl H. Gumbiner.

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Gumbiner, C.H., Hofschire, P.J., Cheatham, J.P. et al. Omphalocele associated with coronary sinus atrial septal defect: Report of two cases. Pediatr Cardiol 11, 167–169 (1990). https://doi.org/10.1007/BF02238851

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Key Words

  • Coronary sinus atrial septal defect
  • Omphalocele