Omphalocele associated with coronary sinus atrial septal defect: Report of two cases


Two children with omphalocele were found to have coronary sinus atrial septal defect as part of their congenital heart disease complex. This unusual atrial communication may elude preoperative detection unless specifically sought. Its occurrence in conjunction with omphalocele may represent more than a chance association.

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Correspondence to Dr. Carl H. Gumbiner.

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Gumbiner, C.H., Hofschire, P.J., Cheatham, J.P. et al. Omphalocele associated with coronary sinus atrial septal defect: Report of two cases. Pediatr Cardiol 11, 167–169 (1990).

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Key Words

  • Coronary sinus atrial septal defect
  • Omphalocele