Summary
Adult-onset Still's disease is an uncommon rheumatological syndrome with a diversity of signs and symptoms. Pulmonary manifestations described are pleuritis and usually transient radiologic infiltrations. The patient presented in this case report had biopsy-proven lung fibrosis when adult-onset Still's disease was diagnosed. Three years after diagnosis, the patient developed clinical signs of the interstitial lung disorder. Radiological and histological progression was observed. Other causes of interstitial lung disorders were excluded. Clinicians should be aware that interstitial lung disease can be a complication of adult-onset Still's disease and can compromise the clinical status of the patient.
This is a preview of subscription content, log in via an institution to check access.
Similar content being viewed by others
References
Bywaters, E.G.L. Still's disease in the adult. Ann Rheum Dis 1971, 30, 121–133.
Reginato, A.J., Schumacher, R.H., Baker, D., et al. Adult onset Still's disease: Experience in 23 patients and literature review with emphasis on organ failure. Semin Arthritis Rheum 1987, 17, 1, 39.
Esdaile, J.M., Tannenbaum, H., Hawkins, D. Adult Still's disease. Am J Med 1980, 68, 825–830.
Ohta, A., Yamaguchi, M., Tsunematsu, T., et al. Adult Still's disease: A multicenter survey of Japanese patients. J Rheumatol 1900, 17, 1058–1063.
Corbett, A.J., Zizic, T.M., Stevens, M.B. Adult-onset Still's disease with an associated restrictive pulmonary defect: a case report. Ann Rheum Dis 1983, 42, 452–454.
Troum, O.M., Mohler, J.G., Koss, M.N., Quismorio, F.S. Pulmonary abnormalities in adult-onset Still's disease (abstract). Arthritis Rheum 1985, 28(suppl), S78.
Cantor, J.P., Pitcher, W.D., Hurd, E. Severe restrictive pulmonary defect in a patient with adult-onset Still's disease. Chest 1987, 92, 939–940.
Liote, H., Liote, F., Lenique, F., Milleron, B.J., Kuntz, D., Akoun, G.M. Adult-onset Still's disease revealed by a pleuropericarditis. Eur Respir J 1990, 3, 1064–1066.
Jottrand, M., Lienart, F., Decaux, G. Manifestations inhabituelles de la maladie de Still de l'adulte. A propos de deux observations. Rev Med Brux 1985, 6, 699–704.
Hirohata, S., Kamoshita, H., Taketani, T., Maeda, S. Adult Still's disease complicated with adult respiratory distress. Arch Intern Med 1986, 146, 2409–2410.
Pedersen, J.E. ARDS — assciated with adult onset Still's disease. Intensive Care Med 1991, 17, 373.
Hay, J.G., Turner-Warwick, M. Interstitial pulmonary fibrosis. In: Textbook of Respiratory Medicine, Eds.: Murray, J.F., Nadel, J.A. Saunders, Philadelphia 1988, 1445–1461.
Author information
Authors and Affiliations
Rights and permissions
About this article
Cite this article
Van Hoeyweghen, R.J., De Clerck, L.S., Van Offel, J.F. et al. Interstitial lung disease and adult-onset still's disease. Clin Rheumatol 12, 418–421 (1993). https://doi.org/10.1007/BF02231592
Received:
Accepted:
Issue Date:
DOI: https://doi.org/10.1007/BF02231592