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Aspects of\(\bar 1\)-inhibitor biochemistry and pathophysiologybiochemistry and pathophysiology

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Summary

During the last few years, the structure and function of humanC \(\bar 1\)-inhibitor have been elucidated. Chromogenic substrate assays for determination ofC \(\bar 1\)-inhibitor activity in plasma are available, and have proved to be of value not only for the diagnosis of hereditary angioedema but also in acquired diseases involvingC \(\bar 1\)-inhibitor, such as cold urticaria and autoimmune disorders as well as acute-phase types of disease states.

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  1. Department of Clinical Chemistry, Umeå University Hospital, S-90185, Umeå, Sweden

    T. K. Nilsson

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Nilsson, T.K. Aspects of\(\bar 1\)-inhibitor biochemistry and pathophysiologybiochemistry and pathophysiology. Clin Rheumatol 6, 332–339 (1987). https://doi.org/10.1007/BF02206831

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