Summary
We describe the case of a woman presenting with a clinical syndrome closely resembling progressive supranuclear palsy, who also showed some progressive neuropsychological defects (aphasia and apraxia) not consistent with a simple loss of timing and activation as is generally postulated in this pathology. The case is discussed with regard to the definition of subcortical dementia and the possible alternative diagnosis of corticobasal degeneration.
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Capitani, E., Laiacona, M. & Barbarotto, R. Progressive neuropsychological and extrapyramidal deterioration resembling progresive supranuclear palsy: is aphasia relevant for correct diagnosis?. Eur Arch Psychiatry Clin Nuerosci 242, 347–351 (1993). https://doi.org/10.1007/BF02190247
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DOI: https://doi.org/10.1007/BF02190247