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Familial superior mesenteric artery syndrome


Five members of a family of eight, including the father and four daughters, presented with symptoms previously attributed to the superior mesenteric artery syndrome. The four daughters also had radiographic studies supporting that diagnosis. This familial clustering raises the possibility of a genetic predisposition to this symptom and radiographic complex.

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Ortiz, C., Cleveland, R.H., Blickman, J.G. et al. Familial superior mesenteric artery syndrome. Pediatr Radiol 20, 588–589 (1990).

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  • Public Health
  • Mesenteric Artery
  • Superior Mesenteric Artery
  • Genetic Predisposition
  • Radiographic Study