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Congenital unilateral pulmonary venous atresia with pulmonary veno-occlusive disease in contralateral lung: An unusual association

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Summary

A patient presenting with the rare association of congenital unilateral pulmonary venous atresia in one lung and pulmonary veno-occlusive disease in the other is described. The patient first presented at the age of 3 ½ years with anemia, hemoptysis, and pulmonary hypertension. After cardiac catheterization and angiocardiography, a diagnosis of atresia of the left pulmonary veins was made for which left pneumonectomy was done. Four years later the patient presented with right-sided congestive failure and radiologic evidence of right-sided pulmonary edema from which death resulted. At autopsy, the right lung showed changes of pulmonary veno-occlusive disease, while the major veins were not involved.

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Authors and Affiliations

  1. Department of Pediatric Cardiology, University of Minnesota, Minneapolis

    Savitri Shrivastava, James H. Moller &  Jesse E. Edwards

  2. Department of Pathology, University of Minnesota, Minneapolis

    Savitri Shrivastava, James H. Moller &  Jesse E. Edwards

  3. Department of Pathology, United Hospital, 333 North Smith Avenue, 55102, St. Paul, Minnesota, USA

    Savitri Shrivastava, James H. Moller &  Jesse E. Edwards

Authors
  1. Savitri Shrivastava
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  2. James H. Moller
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  3. Jesse E. Edwards
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Shrivastava, S., Moller, J.H. & Edwards, J.E. Congenital unilateral pulmonary venous atresia with pulmonary veno-occlusive disease in contralateral lung: An unusual association. Pediatr Cardiol 7, 213–219 (1986). https://doi.org/10.1007/BF02093183

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  • DOI: https://doi.org/10.1007/BF02093183

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