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Small aortic valve annulus in children with fixed subaortic stenosis

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Summary

Twenty-one hearts with fixed subaortic stenosis (FSAS) were examined pathologically. Thirty children with no hemodynamically significant heart disease, 31 children with valvar aortic stenosis, and 25 children with FSAS were studied by echo- and angiocardiography. The following conclusions were drawn: (1) Patients with FSAS often have abnormal aortic valve leaflets as well as small aortic valve annulus. (2) A small aortic annulus/descending aorta ratio is probably present at birth, and may decrease with increasing age. (3) In some patients with FSAS the aortic valve annulus is too small for simple resection of the fibroelastic tissue. A Konno operation is needed for these patients. (4) M-mode echocardiography has not been useful in identifying abnormally small aortic valve annulus in FSAS patients.

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Authors and Affiliations

  1. Heart Institute for Children and The Congenital Heart and Conduction System Center of Christ Hospital and Medical Center, Oak Lawn

    Otto G. Thilenius, Daniel Campbell, Saroja Bharati, Maurice Lev & Rene A. Arcilla

  2. University of Chicago, Chicago, Illinois, USA

    Otto G. Thilenius, Daniel Campbell, Saroja Bharati, Maurice Lev & Rene A. Arcilla

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  1. Otto G. Thilenius
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  2. Daniel Campbell
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  3. Saroja Bharati
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  4. Maurice Lev
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  5. Rene A. Arcilla
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Thilenius, O.G., Campbell, D., Bharati, S. et al. Small aortic valve annulus in children with fixed subaortic stenosis. Pediatr Cardiol 10, 195–198 (1989). https://doi.org/10.1007/BF02083292

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