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Westphal-Strümpell disease: A case report with a new method of urinary copper evaluation

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Abstract

A case of Westphal-Strümpell disease diagnosed by classical serum and urinary investigations is described.

The efficacy of specific treatment was monitored by the values of urinary copper excretion, determined by a new quantitative chemical method, which is described in detail.

Sommario

Gli Autori riferiscono a proposito di un caso di malattia di Westphal-Strumpell. La diagnosi è stata fatta sulla base dei dati plasmatici (ceruloplasmina, cupremia) e della cupruria.

L'efficacia del trattamento specifico è stata moniototrizzata con i valori della cupruria. Quest'ultima è stata misurata con un nuovo metodo chimico quantitativo, descritto in dettaglio.

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References

  1. Beyer W.:Spectrophotometric determination of copper in serum, urine and feces. Clin. Chim. Acta, 38: 119–126, 1972.

    Article  PubMed  Google Scholar 

  2. Boudin G., Pepin B.V.:Dégénérescense hépatolenticulaire. Masson et Cie Paris, 1959.

    Google Scholar 

  3. Czlokowska A., Rodo N.:Late onset of Wilson's disease. Report of a family. Arch. Neurol., 38: 729–739, 1981.

    PubMed  Google Scholar 

  4. Fitzgerald M., Gross J., Goldstein N., Wahner H., McCall J.:Wilson's disease (hepatolenticular degeneration) of adult onset. Report of a case. Mayo Clin. Proc., 50: 438–442, 1975.

    PubMed  Google Scholar 

  5. Martin J.P.: Wilson's disease. In Vinken P.J. and Bruyn G.W. (Eds.): Handbook of Clinical Neurology. North Holland Publ. Co., Amsterdam, Vol. 6, 267–278, 1968.

    Google Scholar 

  6. Sternlieb J., Scheinberg H.:Prevention of Wilson's disease in asymptomatic patients. N. Engl. J. Med., 278: 352–359, 1968.

    PubMed  Google Scholar 

  7. Metodi di analisi cliniche per spettroscopia di assorbimento atomico. Pages AA-Cu 1, 1–1. Perkin-Elmer, Norwalk, Connecticut, U.S.A.

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Authors and Affiliations

  1. Istituto di Neurologica, Università Cattolica, Roma

    Stefanini M. C. & Altavista M. C.

  2. Istituto di Medicina del Lavoro, Università Cattolica, Roma

    Carelli G.

Authors
  1. Stefanini M. C.
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  2. Altavista M. C.
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  3. Carelli G.
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Stefanini, M.C., Altavista, M.C. & Carelli, G. Westphal-Strümpell disease: A case report with a new method of urinary copper evaluation. Ital J Neuro Sci 4, 197–202 (1983). https://doi.org/10.1007/BF02043905

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  • DOI: https://doi.org/10.1007/BF02043905

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