Pediatric Radiology

, Volume 21, Issue 6, pp 445–446 | Cite as

Rhabdomyosarcoma associated with familial adenomatous polyposis

  • S. J. Armstrong
  • A. W. Duncan
  • M. G. Mott
Short Reports


We report a case of a 16 year old girl with orbital rhabdomyosarcoma who during chemotherapy developed bloody diarrhoea. On investigation she was found to have multiple colonic polyps. Cytogenetic analysis has shown a pattern typical of familial adenomatous polyposis. We present a review of the literature concerning the associations of familial adenomatous polyposis. The association of familial adenomatous polyposis with rhabdomyosarcoma has not been previously reported.


Public Health Familial Adenomatous Polyposis Cytogenetic Analysis Rhabdomyosarcoma Colonic Polyp 
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Copyright information

© Springer-Verlag 1991

Authors and Affiliations

  • S. J. Armstrong
    • 1
  • A. W. Duncan
    • 1
  • M. G. Mott
    • 2
  1. 1.Department of RadiodiagnosisBristol Royal Hospital for Sick ChildrenBristolUK
  2. 2.Department of Paediatric OncologyBristol Royal Hospital for Sick ChildrenBristolUK

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