Pediatric Radiology

, Volume 24, Issue 2, pp 145–146 | Cite as

Colonic hamartomatous polyposis associated with hypertrophic osteoarthropathy

  • P. E. Erkul
  • O. M. Ariyürek
  • D. Altinok
  • A. Bakkaloĝlu
  • E. Kotiloĝlu
Short Reports

Abstract

A 7-year-old girl with an unremarkable family history was admitted with complaints of diarrhea containing mucus and blood, abdominal pain, weight loss and fever for 10 months. Although her symptoms, physical examination and laboratory results were highly suggestive of inflammatory bowel disease, radiologic studies and colonoscopy demonstrated multiple colonic polyps. A bilateral and symmetric lamellar periosteal reaction and osteopenia were present on her extremity radiographs. The chest radiograph and thoracic CT scan were normal. The histologic nature of the polyps was determined as hamartoma. One month after subtotal colectomy, the patient's symptoms resolved and she gained 7kg in weight. The association of generalized juvenile polyposis and hypertrophic osteoarthropathy has previously been described in five cases; arteriovenous malformations were present in four of them. In our case the polyps were hamartomatous and localized in the colon, without associated arteriovenous malformation.

Keywords

Family History Diarrhea Abdominal Pain Inflammatory Bowel Disease Bowel Disease 

References

  1. 1.
    Cox KL, Frates RC, Wong A et al (1980) Hereditary generalized juvenile polyposis associated with pulmonary arteriovenous malformation. Gastroenterology 78: 1566PubMedGoogle Scholar
  2. 2.
    Baert AL, Casteels-Van Daele, Broeckx J et al (1983) Generalized juvenile polyposis with pulmonary arteriovenous malformations and hypertrophic osteoarthropathy. AJR 141: 661PubMedGoogle Scholar
  3. 3.
    Prieto G, Polanco I, Sarria J, Larrauri J, Lassaletta L (1990) Association of juvenile and adenomatous polyposis with pulmonary arteriovenous malformation and hypertrophic osteoarthropathy. J Pediatr Gastroenterol Nutrition 11: 133Google Scholar
  4. 4.
    Simpson EL, Dalinka MK (1985) Association of hypertrophic osteoarthropathy with gastrointestinal polyposis. AJR 144: 983PubMedGoogle Scholar
  5. 5.
    Bulow S (1984) Colorectal polyposis syndromes. Scand J Gastroenterol 19: 289PubMedGoogle Scholar

Copyright information

© Springer-Verlag 1994

Authors and Affiliations

  • P. E. Erkul
    • 1
  • O. M. Ariyürek
    • 2
  • D. Altinok
    • 2
  • A. Bakkaloĝlu
    • 1
  • E. Kotiloĝlu
    • 3
  1. 1.Department of PediatricsHacettepe UniversityAnkaraTurkey
  2. 2.Department of RadiologyHacettepe UniversityAnkaraTurkey
  3. 3.Department of PathologyHacettepe UniversityAnkaraTurkey

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