Pediatric Radiology

, Volume 24, Issue 1, pp 66–67 | Cite as

Neurofibromatosis type 1 involving the liver: Ultrasound and CT manifestations

  • Y. Kakitsubata
  • S. Kakitsubata
  • T. Sonoda
  • K. Watanabe
Short Reports


We present a rare case of neurofibromatosis type 1 (NF-1) involving the liver in a 15-year-old girl. Abdominal ultrasonography revealed infiltrative hypoechoic masses around the porta hepatis and intrahepatic portal branches. CT also revealed extensive low-attenuation masses in the hepatic hilum and retroperitoneum. The tumor spread into the liver along the portal vein. It should be borne in mind that the liver may be involved by neurofibromas in patients with NF-1.


Public Health Portal Vein Rare Case Abdominal Ultrasonography Neurofibromatosis 
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Copyright information

© Springer-Verlag 1994

Authors and Affiliations

  • Y. Kakitsubata
    • 1
  • S. Kakitsubata
    • 1
  • T. Sonoda
    • 2
  • K. Watanabe
    • 1
  1. 1.Department of RadiologyMiyazaki Medical CollegeMiyazakiJapan
  2. 2.Department of PediatricsMiyazaki Medical CollegeMiyazakiJapan

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