Pediatric Radiology

, Volume 21, Issue 7, pp 508–510 | Cite as

Radio-ulnar synostosis in Williams syndrome

A frequently associated anomaly
  • K. A. Charvat
  • L. Hornstein
  • A. E. Oestreich


Limitation of supination and pronation of the forearm has been occasionally described in individuals with Williams syndrome. It was found in 26% of 23 subjects examined, and was associated with a spectrum of severity of radio-ulnar synostosis on radiography. The occurrence of this functional motor impairment in a substantial subset of persons with Williams syndrome is relevant, because its evaluation is important in habilitation planning.


Public Health Motor Impairment Williams Syndrome Synostosis Functional Motor 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.


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Copyright information

© Springer-Verlag 1991

Authors and Affiliations

  • K. A. Charvat
    • 1
    • 2
  • L. Hornstein
    • 1
    • 2
  • A. E. Oestreich
    • 3
  1. 1.Cincinnati Center for Developmental DisordersChildren's Hospital Medical CenterCincinnatiUSA
  2. 2.Department of PediatricsChildren's Hospital Medical CenterCincinnatiUSA
  3. 3.Department of RadiologyChildren's Hospital Medical Center and University of CincinnatiCincinnatiUSA

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