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Primary progressive aphasia: description of a clinical case with nine years of follow-up

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Abstract

We describe the case of a woman with primary progressive aphasia who, over a period of nine years, has shown no signs of clinical deterioration and has only a symptomatic language disturbance. Neuropsychological follow-up has revealed progressive language impairment, with the integrity of praxis, visuoperceptive gnosia and short term visuospatial memory remaining intact; the only impairment was that revealed by long-term memory tests.

Sommario

Descriviamo il caso di una donna affetta da primary progressive aphasia: nell'arco di nove anni la paziente non ha evidenziato segni di deterioramento clinico, rimanendo come unico sintomo il disturbo del linguaggio. Il follow-up neuropsicologico ha dimostrato la progressiva compromissione del linguaggio e l'integrità di prassie, gnosie visuopercettive e memoria visuo-spaziale a breve termine, con compromissione delle sole prove di memoria a lungo termine.

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Mazzoni, M., Pollera, O.M. & Giraldi, C. Primary progressive aphasia: description of a clinical case with nine years of follow-up. Ital J Neuro Sci 17, 161–165 (1996). https://doi.org/10.1007/BF02000849

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