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European Journal of Pediatrics

, Volume 153, Issue 2, pp 100–102 | Cite as

Imaging diagnosis and follow-up of infantile hepatic haemangioendothelioma: A case report

  • Thomas M. Berger
  • Markus F. Berger
  • Alan D. Hoffman
  • Donald Zimmerman
  • Otmar Tönz
Hematology/Oncology Original Paper

Abstract

A 4-week-old male infant was admitted to the hospital with acute gastrointestinal bleeding and marked coagulopathy secondary to vitamin K malabsorption in the presence of cholestasis. Physical examination revealed hepatomegaly and cutaneous haemangiomas. Ultrasonography, CT, and MRI demonstrated a multifocal vascular process and allowed the diagnosis of infantile hepatic haemangioendothelioma to be made without the use of more invasive diagnostic procedures. To avoid high-output congestive heart failure, the patient was treated with oral corticosteroids. After 5 months, rapid involution of the vascular malformations ensued. At age 2 years, a magnetic resonance scan confirmed complete resolution of the hepatic haemangioendothelioma.

Key words

CT Infantile hepatic haemangioendothelioma MRI Ultrasonography 

Abbreviation

IHH

infantile hepatic haemangioendothelioma

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Copyright information

© Springer-Verlag 1994

Authors and Affiliations

  • Thomas M. Berger
    • 1
    • 2
  • Markus F. Berger
    • 3
  • Alan D. Hoffman
    • 4
  • Donald Zimmerman
    • 5
  • Otmar Tönz
    • 1
  1. 1.Department of PaediatricsChildren's Hospital of LucerneLucerneSwitzerland
  2. 2.Children's Hospital, Joint Program in NeonatologyBostonUSA
  3. 3.Institute of Diagnostic RadiologyCantonal HospitalAarauSwitzerland
  4. 4.Department of Diagnostic RadiologyMayo Clinic and Mayo FoundationRochesterUSA
  5. 5.Department of PaediatricsMayo Clinic and Mayo FoundationRochesterUSA

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