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European Journal of Pediatrics

, Volume 149, Issue 11, pp 779–780 | Cite as

Intravenous immunoglobulin in Diamond-Blackfan anaemia

  • S. Miceli Sopo
  • M. A. Pesaresi
  • M. Pastore
  • A. Stabile
Hematology/Oncology

Abstract

Since immunological disorders have been demonstrated in patients with Diamond-Blackfan anaemia (DBA), intravenous immunoglobulins (IVIG) were administered to a 14-year-old girl with DBA and congenital malformations, previously treated with corticosteroids and blood transfusions. No therapeutic effect was observed.

Key words

Congenital pure red cell aplasia Diamond-Blackfan anaemia Intravenous immunoglobulin 

Abbreviations

DBA

Diamond-Blackfan anaemia

hrIL-2

human recombinant interleukin 2

IVIG

intravenous immunoglobulins

PBMC

peripheral blood mononuclear cells

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Copyright information

© Springer-Verlag 1990

Authors and Affiliations

  • S. Miceli Sopo
    • 1
  • M. A. Pesaresi
    • 1
  • M. Pastore
    • 1
  • A. Stabile
    • 1
  1. 1.Department of PaediatricsCatholic University of RomeRomeItaly

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