Intravenous immunoglobulin in Diamond-Blackfan anaemia
Since immunological disorders have been demonstrated in patients with Diamond-Blackfan anaemia (DBA), intravenous immunoglobulins (IVIG) were administered to a 14-year-old girl with DBA and congenital malformations, previously treated with corticosteroids and blood transfusions. No therapeutic effect was observed.
Key wordsCongenital pure red cell aplasia Diamond-Blackfan anaemia Intravenous immunoglobulin
human recombinant interleukin 2
peripheral blood mononuclear cells
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