Advertisement

Journal of Inherited Metabolic Disease

, Volume 10, Supplement 2, pp 329–332 | Cite as

Lipid abnormalities in Batten's disease

  • W. S. Gillis
  • M. J. Bennett
  • J. H. Galloway
  • I. J. Cartwright
  • G. P. Hosking
  • C. M. L. Smith
Short Communication

Keywords

Public Health Lipid Internal Medicine Metabolic Disease Lipid Abnormality 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

Preview

Unable to display preview. Download preview PDF.

Unable to display preview. Download preview PDF.

References

  1. Bennett, M. J., Gillis, W. S., Hosking, G. P., Galloway, J. H. and Cartwright, I. J. Lipid abnormalities in serum in Batten's disease.Develop. Med. Child. Neurol. 28 (1986) 815–817PubMedGoogle Scholar
  2. Bennett, M. J., Mathers, N. J., Hemming, F. W., Zweije-Hofman, I. and Hosking, G. P. Urinary sediment dolichol excretion in patients with Batten's disease and other neuro-degenerative and storage disorders.Paediatr. Res. 19 (1985) 213–216Google Scholar
  3. Cartwright, I. J., Lockley, A. G., Galloway, J. H., Greaves, M. and Preston, F. E. The effect of dietaryω-3 polyunsaturated fatty acids on erythrocyte membrane phospholipids, erythrocyte deformability and blood viscosity in healthy volunteers.Atherosclerosis 55 (1985) 267–281PubMedGoogle Scholar
  4. Egeshor-Jensen, G. and Clausen, J. Leucocyte glutathione peroxidase activity and selenium levels in Batten's disease.Scand. J. Clin. Lab. Invest. 43 (1983) 187–196PubMedGoogle Scholar
  5. Fleischer, S. and Anderson, R. E. Chemistry and metabolism of lipids in the vertebrate retina.Prog. Lipid Res. 22 (1983) 79–131PubMedGoogle Scholar
  6. Galloway, J. H., Cartwright, I. J., Woodcock, B. E., Greaves, M., Russell, R. G. G. and Preston, F. E. Effects of dietary supplementation on the fatty acid composition of the human platelet membrane; demonstration of selectivity in the incorporation of eicosapentanoic acid into membrane phospholipid pools.Clin. Sci. 68 (1985) 449–454PubMedGoogle Scholar
  7. Mangold, H. K. Aliphatic lipids. In Stahl, E. (ed.)Thin Layer Chromatography, Academic Press, London, 1965, pp. 137–186Google Scholar
  8. Ng Ying Kim, N. M. K., Palo, J., Haltia, M. and Wolfe, L. S. High levels of brain dolichols in neuronal ceroid-lipofucinosis and senescence.J. Neurochem. 40 (1983) 1465–1473PubMedGoogle Scholar
  9. Pagnan, A., Zanetti, G., Braggion, M., Ziran, L., Lusiani, L., Visona, A., Castellani, V. and Ronsivalle, G. The double pre-beta very low density lipoprotein lipoproteinaemia (DPBL): a new dyslipoproteinaemic state.Diabet. Metab. 11 (1985) 343–349Google Scholar
  10. Paton, B. C. and Poulos, A. Dolichol metabolism in cultured skin fibroblasts from patients with neuronal ceroid-lipofucinosis (Batten's disease).J. Inher. Metab. Dis. 7 (1984) 112–116PubMedGoogle Scholar

Copyright information

© SSIEM and MTP Press Limited 1987

Authors and Affiliations

  • W. S. Gillis
    • 1
  • M. J. Bennett
    • 1
  • J. H. Galloway
    • 3
  • I. J. Cartwright
    • 4
  • G. P. Hosking
    • 2
  • C. M. L. Smith
    • 5
  1. 1.Department of Chemical PathologySheffield Children's HospitalSheffieldUK
  2. 2.Ryegate CentreSheffield Children's HospitalSheffieldUK
  3. 3.Department of Human Metabolism and Clinical BiochemistryThe Royal Hallamshire HospitalSheffieldUK
  4. 4.Department of HaematologyThe Royal Hallamshire HospitalSheffieldUK
  5. 5.Department of NeuropathologyThe Royal Hallamshire HospitalSheffieldUK

Personalised recommendations