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Biochemical evidence of carnitine effect on propionate elimination

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Journal of Inherited Metabolic Disease

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References

  • Bohmer, T. and Bremer, J. Propionylcarnitine: Physiological variationsin vivo.Biochim. Biophys. Acta 152 (1968) 559–567

    PubMed  Google Scholar 

  • Gompertz, D., Goodey, P.A., Thom, H., Russell, G., Johnston, A. W., Mellor, D. H., MacLean, M. W., Ferguson-Smith, M. E. and Ferguson-Smith, M. A. Perinatal diagnosis and family studies in case of propionicacidaemia.Clin. Genet. 8 (1975) 244–250

    PubMed  Google Scholar 

  • Roe, C. R. and Bohan, T. P.l-Carnitine therapy in propionicacidaemia.Lancet 1 (1982) 1411–1412

    PubMed  Google Scholar 

  • Rosenberg, L. E. Disorders of propionate and methylmalonate metabolism. In Stanbury, J. B., Wyngaarden, J. B., Fredrickson, D. S., Goldstein, J. L. and Brown, M. S. (eds.)The Metabolic Basis of Inherited Disease, 5th edn., McGraw-Hill, New York, 1983, pp. 474–497

    Google Scholar 

  • Satoh, T., Narisawa, K., Tazawa, Y., Suzuki, H., Hayasaka, K., Tada, K. and Kawakami, T. Dietary therapy in a girl with propionic acidaemia: Supplement with leucine resulted in catch up growth.Tohoku J. Exp. Med. 139 (1983) 411–415

    PubMed  Google Scholar 

  • Sugiyama, N., Wada, Y., Morishita, H. and Nonaka, I. Different ketogenic response to medium-chain triglycerides and to long-chain triglycerides in a case of muscular carnitine palmitoyltransferase deficiency.J. Inher. Metab. Dis. 5 (1982) 233–234

    PubMed  Google Scholar 

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Authors and Affiliations

  1. Department of Medicine and Pediatrics, School of Dentistry, Aichi-Gakuin University, Suemori-dohri, Chikusa-ku, 464, Nagoya, Japan

    N. Sugiyama

  2. Department of Pediatrics, Nagoya City University, Medical School, Kawasumi-cho, Mizuho-ku, 467, Nagoya, Japan

    H. Morishita, S. Nagaya, T. Nakajima, A. Kawase, A. Ohya, S. Sugiyama, K. Kamiya, I. Watanabe, H. Togari, M. Kobayashi, Y. Ogawa & Y. Wada

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  1. N. Sugiyama
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  2. H. Morishita
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  3. S. Nagaya
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  4. T. Nakajima
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  5. A. Kawase
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  6. A. Ohya
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  7. S. Sugiyama
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  8. K. Kamiya
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  9. I. Watanabe
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  10. H. Togari
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  11. M. Kobayashi
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  12. Y. Ogawa
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  13. Y. Wada
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Sugiyama, N., Morishita, H., Nagaya, S. et al. Biochemical evidence of carnitine effect on propionate elimination. J Inherit Metab Dis 7, 137–138 (1984). https://doi.org/10.1007/BF01801775

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  • DOI: https://doi.org/10.1007/BF01801775

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