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Alloisoleucine in isovaleric acidaemia

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Journal of Inherited Metabolic Disease

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References

  • Matthews, D. E., Ben-Galim, E., Haymond, M. W. and Bier, D. M. Alloisoleucine formation in maple syrup urine disease: isotopic evidence for the mechanism.Pediatr. Res. 14 (1980) 854–857

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  • Pettit, F. H., Yeamen, S. H. and Reed, L. J. Purification and characterization of branchedchain α-keto acid dehydrogenase complex of bovine kidney.Proc. Natl Acad. Sci. USA. 75 (1978) 4881–4885

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Authors and Affiliations

  1. Laboratoire de Biochimie Médicale B, Hôpital Necker Enfants Malades, 149, rue de Sévres, 75743, Paris Cedex 15, France

    D. Rabier, P. Parvy, J. Bardet & P. Kamoun

  2. Department de Génétique Médicale, Hôpital Necker Enfants Malades, 149, rue de Sévres, 75743, Paris Cedex 15, France

    J. M. Saudubray

Authors
  1. D. Rabier
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  2. P. Parvy
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  3. J. Bardet
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  4. J. M. Saudubray
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  5. P. Kamoun
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Rabier, D., Parvy, P., Bardet, J. et al. Alloisoleucine in isovaleric acidaemia. J Inherit Metab Dis 15, 154–155 (1992). https://doi.org/10.1007/BF01800358

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  • DOI: https://doi.org/10.1007/BF01800358

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