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Journal of Inherited Metabolic Disease

, Volume 10, Issue 3, pp 297–300 | Cite as

Biosynthesis of peroxisomal membrane polypeptides in infants with Zellweger syndrome

  • Y. Suzuki
  • N. Shimozawa
  • T. Orii
  • J. Aikawa
  • K. Tada
  • T. Kuwabara
  • T. Hashimoto
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Keywords

Public Health Internal Medicine Polypeptide Metabolic Disease Peroxisomal Membrane 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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References

  1. Datta, N. S., Wilson, G. N. and Hajra, A. K. Deficiency of enzymes catalyzing the biosynthesis of glycerol-ether lipids in Zellweger syndrome.N. Engl. J. Med. 311 (1984) 1080–1083Google Scholar
  2. Fujiki, Y., Hubbard, A. L., Lowler, S. and Lazarow, P. B. Isolation of intracellular membranes by means of sodium carbonate treatment: application to endoplasmic reticulum.J. Cell Biol. 93 (1982) 97–102Google Scholar
  3. Goldfischer, S., Collins, J., Rapin, I., Neumann, P., Neglia, W., Spiro, A. J., Ishiil, T., Roels, F., Vamecq, J. and Van Hoof, F. Pseudo-Zellweger syndrome: deficiencies in several peroxisomal oxidative activities.J. Pediatr. 108 (1986) 25–32Google Scholar
  4. Hashimoto, T., Kuwabara, T., Usuda, N. and Nagata, T. Purification of membrane polypeptides of rat liver peroxisomes.J. Biochem, (Tokyo) 100 (1986) 301–310Google Scholar
  5. Mori, M., Miura, S., Tatibana, M. and Cohen, P. P. Cell-free translation of carbamyl phosphate synthetase I and ornithine transcarbamylase messenger RNAs of rat liver.J. Biol. Chem. 256 (1981) 4127–4132Google Scholar
  6. Poulos, A., van Crugten, C., Sharp, P., Carey, W. F., Robertson, E., Becroft, D. M. O., Saudubray, J. M., Poll-The, B. T., Christensen, E. and Brandt, N. Prenatal diagnosis of Zellweger syndrome and related disorders: impaired degradation of phytanic acid.Eur. J. Pediatr. 145 (1986) 507–510Google Scholar
  7. Schutgens, R. B. H., Heymans, H. S. A., Wanders R. J. A., Bosh, H. v. d. and Tager, J. M. Peroxisomal disorders: a newly recognized group of genetic diseases.Eur. J. Pediatr. 144 (1986) 430–440Google Scholar
  8. Suzuki, Y., Orii, T., Mori, M., Tatibana, M. and Hashimoto, T. Deficient activities and proteins of peroxisomal β-oxidation enzymes in infants with Zellweger syndrome.Clin. Chim. Acta 156 (1986a) 191–196Google Scholar
  9. Suzuki, Y., Orii, T. and Hashimoto, T. Biosynthesis of peroxisomal β-oxidation enzymes in infants with Zellweger syndrome.J. Inher. Metab. Dis. 9 (1986b) 292–296Google Scholar
  10. Suzuki, Y., Orii, T., Takiguchi, M., Mori, M., Hijikata, M. and Hashimoto, T. Biosynthesis of membrane polypeptides of rat liver peroxisomes.J. Biochem. (Tokyo) 101 (1987) 491–496Google Scholar

Copyright information

© SSIEM and MTP Press Limited 1987

Authors and Affiliations

  • Y. Suzuki
    • 1
  • N. Shimozawa
    • 1
  • T. Orii
    • 1
  • J. Aikawa
    • 2
  • K. Tada
    • 2
  • T. Kuwabara
    • 3
  • T. Hashimoto
    • 3
  1. 1.Department of PaediatricsGifu University School of MedicineGifuJapan
  2. 2.Department of PaediatricsTohoku University School of MedicineSendaiJapan
  3. 3.Department of BiochemistryShinshu University School of MedicineMatsumotoJapan

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