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Journal of Inherited Metabolic Disease

, Volume 5, Issue 2, pp 111–113 | Cite as

Normal hydroxylation of proline in collagen synthesized by skin fibroblasts from a patient with prolidase deficiency

  • P. M. Royce
  • D. M. Danks
Article

Abstract

The extent of hydroxylation of proline in collagen synthesized and secreted into the culture medium by skin fibroblasts derived from a patient with prolidase deficiency has been examined and found to be normal. It would seem likely that to a considerable extent the urinary proline-containing dipeptides apparent in this condition are derived from sources other than collagen.

Keywords

Public Health Collagen Internal Medicine Proline Metabolic Disease 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© MTP Press Limited 1982

Authors and Affiliations

  • P. M. Royce
    • 1
  • D. M. Danks
    • 1
    • 2
  1. 1.Genetics Research UnitRoyal Children's Hospital Research FoundationParkvilleAustrialia
  2. 2.Department of PaediatricsUniversity of MelbourneParkvilleAustralia

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