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Long-term cornstarch therapy in glycogen storage disease types I, Ib and III

  • R. Gatti
  • G. Lamedica
  • M. Di Rocco
  • D. Massocco
  • N. Marchese
  • C. Borrone
Short Communication

Keywords

Cornstarch Glycogen Storage Disease Glycogen Storage Disease Type Accelerate Growth Rate Uncooked Cornstarch 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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References

  1. Burr, I. N., O'Neall, T. A., Karson, D. B., Howard, L. J. and Green, H. L. Comparison of the effect of total enteral nutrition, continuous intragastric feeding and portocaval shunt on a patient with type I glycogen storage disease.J. Pediatr. 85 (1979) 792Google Scholar
  2. Chen, Y. T., Cornblath, M. and Sidbury, T. B. Cornstarch therapy in type I glycogen storage disease.N. Engl. J. Med. 310 (1984) 171PubMedCrossRefGoogle Scholar
  3. Fernandes, J., Berger, R. and Smit, G. P. A. Lactate as a cerebral meta10545c fuel for glucose-6-phosphatase deficient children.Pediatr. Res. 18 (1984a) 335PubMedCrossRefGoogle Scholar
  4. Fernandes, J., Smit, G. P. A. and Berger, R. Dietary treatment of children with liver glycogenosis. In Benson, P. F. (ed.)Screening and Management of Potentially Treatable Genetic Meta10545c Disorders. MTP Press, Lancaster, 1984b, pp. 161–176Google Scholar
  5. Greene, H. L., Slonin, A. E., Burr, J. M. and Moran, R. Type I glycogen storage disease: five years of management with nocturnal intragastric feeding.J. Pediatr. 96 (1980) 590PubMedCrossRefGoogle Scholar
  6. Sloan, H. R. and Zipt, W. B. Cornstarch therapy of glycogen storage disease type I (GSD I).Pediatr. Res. 17 (1983) 220AGoogle Scholar
  7. Smit, G. P. A., Boyer, R., Potasmick, R., Morer, S. W and Fernandes, J. The dietary treatment of children with type I glycogen storage disease with slow release carbohydrate.Pediatr. Res. 18 (1984) 879PubMedCrossRefGoogle Scholar

Copyright information

© SSIEM and MTP Press Limited 1986

Authors and Affiliations

  • R. Gatti
    • 1
  • G. Lamedica
    • 2
  • M. Di Rocco
    • 1
  • D. Massocco
    • 1
  • N. Marchese
    • 2
  • C. Borrone
    • 1
  1. 1.III Divisione di PediatriaIstituto ‘G. Gaslini’GenoaItaly
  2. 2.Laboratorio di Chimica ClinicaIstituto ‘G. Gaslini’GenoaItaly

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