Journal of Inherited Metabolic Disease

, Volume 10, Issue 1, pp 28–32 | Cite as

Normal dolichol concentration in urine sediments from four patients with neuronal ceroid lipofuscinosis (Batten's disease)

  • B. C. Paton
  • A. Poulos


The dolichol contents of urine sediments from a patient with infantile (Santavuori), a patient with late infantile (Jansky-Bielschowsky) and two patients with juvenile (Spielmeyer-Vogt) neuronal ceroid lipofuscinosis (Batten's disease) were not elevated when compared to those from healthy controls.


Public Health Internal Medicine Metabolic Disease Urine Sediment Neuronal Ceroid Lipofuscinosis 
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Copyright information

© SSIEM and MTP Press Limited 1987

Authors and Affiliations

  • B. C. Paton
    • 1
  • A. Poulos
    • 1
  1. 1.Department of Chemical PathologyThe Adelaide Children's HospitalNorth Adelaide

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