Journal of Inherited Metabolic Disease

, Volume 19, Issue 2, pp 130–132 | Cite as

Decreased activity of the mitochondrial ATP-synthase in fibroblasts from children with late-infantile and juvenile neuronal ceroid lipofuscinosis

  • A. M. Das
  • A. Kohlschütter
Short Communication


Public Health Internal Medicine Metabolic Disease Neuronal Ceroid Lipofuscinosis Juvenile Neuronal Ceroid Lipofuscinosis 
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Copyright information

© SSIEM and Kluwer Academic Publishers 1996

Authors and Affiliations

  • A. M. Das
    • 2
  • A. Kohlschütter
    • 1
  1. 1.Department of PediatricsUniversity of HamburgHamburgGermany
  2. 2.Department of Pediatric Nephrology and Metabolic DisordersKinderklinik der Medizinischen Hochschule HannoverHannoverGermany

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